Scleroderma Patients with Pulmonary Artery Hypertension: A Case Report

Muhammad Miftahussurur, Joewono Soeroso

Abstract

Scleroderma or systemic sclerosis (SSc) is a multiorgan connective tissue disorder involving the skin, lungs, heart, digestive tract, musculoskeletal system, and peripheral circulation. Pulmonary arterial hypertension (PAH) is an increase in mean pulmonary artery pressure > 25 mmHg as measured by echocardiography or catheterization. The incidence of PAHs with SSc is so rare that reports, in this case, are necessary. Objective: to describe the management of PAH patients with SSc. Case: a 32-year-old patient experiencing PAHs with SSc has stiffness of the mouth and is difficult to open. The ECG shows a sinus tachycardia with a Right axis destination and a cardiomegaly thorax photo with a 64% cardio-thorax ratio. Some clinical data show autoimmunity. Treatment is oxygen, diuretic, thrombolytic, and immunosuppressive drugs. Conclusions: Reports of PAH treatment with SSC are essential for the improvement of therapy

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Paper Citation


in Harvard Style

Miftahussurur M. and Soeroso J. (2017). Scleroderma Patients with Pulmonary Artery Hypertension: A Case Report.In Proceedings of the International Meeting on Regenerative Medicine - Volume 1: IMRM, ISBN 978-989-758-334-6, pages 413-419. DOI: 10.5220/0007322404130419


in Bibtex Style

@conference{imrm17,
author={Muhammad Miftahussurur and Joewono Soeroso},
title={Scleroderma Patients with Pulmonary Artery Hypertension: A Case Report},
booktitle={Proceedings of the International Meeting on Regenerative Medicine - Volume 1: IMRM,},
year={2017},
pages={413-419},
publisher={SciTePress},
organization={INSTICC},
doi={10.5220/0007322404130419},
isbn={978-989-758-334-6},
}


in EndNote Style

TY - CONF

JO - Proceedings of the International Meeting on Regenerative Medicine - Volume 1: IMRM,
TI - Scleroderma Patients with Pulmonary Artery Hypertension: A Case Report
SN - 978-989-758-334-6
AU - Miftahussurur M.
AU - Soeroso J.
PY - 2017
SP - 413
EP - 419
DO - 10.5220/0007322404130419