Serial Excisions of Three Big Tumors on the Upper Right Side of Nose, Left Nostril, and Right Side of Chin of NF 1 under Tumescent Surgical Anesthesia in a Woman

Sri Lestari, Fesdia Sari, Nadya Hasriningrum, Elsi Kemala Putri, Yulia Eka Suryani

2018

Abstract

Background: Neurofibromatosis type-1 (NF1) is autosomal dominant and multi-system disorders. An incidence 1 in 3000 live births. There are three big tumors on the face that could disturb function organs around the tumors and she wanted to remove that tumors. Case report: A case of 32-year-old woman with chief complaint there were brownish patches and bumps that painless and not itchy on the most part of the body since 20 years ago. At the age of 10 year-old there were appeared multiple skin colour bumps and growing bigger all over the body. On physical examination there were multiple skin colour tumors on most of the body, three big tumors on upper right side of nose, left nostril, and right side of chin, caféau-lait spots, generalized distribution, disseminated. We consulted to Ophtalmologic Departement there were Lish’s nodules on iris of her eyes, on Neurology Departement no neurologycal focal defisits were found. Histopathological examination is neurofibroma. We excised three big tumors on the upper right side of nose, left nostril, and right side of chin with eliptical, subcutaneous tissue pedicle island flap and long inferiorly melolabial transposition flap designs under tumescent surgical anesthesia and there were good cosmetic result. Discussion: NF-1 is best cared for within a multidisciplinary approach, which has access to a wide range of subspecialists. We excised three big tumors on upper right side of nose, left nostril, and right side of chin every two-weeks to maintanance function of organ with good cosmetic result.

Paper Citation

in Harvard Style

Lestari S., Sari F., Hasriningrum N., Putri E. and Suryani Y. (2018). Serial Excisions of Three Big Tumors on the Upper Right Side of Nose, Left Nostril, and Right Side of Chin of NF 1 under Tumescent Surgical Anesthesia in a Woman.In Proceedings of the 23rd Regional Conference of Dermatology - Volume 1: RCD, ISBN 978-989-758-494-7, pages 411-414. DOI: 10.5220/0008158604110414

in Bibtex Style

@conference{rcd18,
author={Sri Lestari and Fesdia Sari and Nadya Hasriningrum and Elsi Kemala Putri and Yulia Eka Suryani},
title={Serial Excisions of Three Big Tumors on the Upper Right Side of Nose, Left Nostril, and Right Side of Chin of NF 1 under Tumescent Surgical Anesthesia in a Woman},
booktitle={Proceedings of the 23rd Regional Conference of Dermatology - Volume 1: RCD,},
year={2018},
pages={411-414},
publisher={SciTePress},
organization={INSTICC},
doi={10.5220/0008158604110414},
isbn={978-989-758-494-7},
}

in EndNote Style

TY - CONF

JO - Proceedings of the 23rd Regional Conference of Dermatology - Volume 1: RCD,
TI - Serial Excisions of Three Big Tumors on the Upper Right Side of Nose, Left Nostril, and Right Side of Chin of NF 1 under Tumescent Surgical Anesthesia in a Woman
SN - 978-989-758-494-7
AU - Lestari S.
AU - Sari F.
AU - Hasriningrum N.
AU - Putri E.
AU - Suryani Y.
PY - 2018
SP - 411
EP - 414
DO - 10.5220/0008158604110414