Vogt Koyanagi Harada Syndrome

Ernawati Hidayat, Milka Wulansari, Yosep Ferdinand Rahmat Sugianto, Galih Sari Damayanti, Dewi Kusuma Astutik

2019

Abstract

Vogt-Koyanagi-Harada syndrome (VKHS) is a rare autoimmune disorder involving pigmented multiorgan. VKHS reported 6-8% in Asia,1-4 % in North America, and 2-4 % in Brazil of all uveitis.Diagnosis is made based on American Uveitis Society (AUS) criteria; no history of eye trauma, and minimum 3 of 4 signs: bilateral chronic iridocyclitis, uveitis, neurologic signs (tinnitus, neck stiffness, CNS symptoms), and dermatologic signs (alopecia, poliosis, vitiligo). A 51-year-old female presented with generalized hypopigmented-non pruritic patches since 8-year-old. Visual impairment was reported one month before. Patches of white hair were found on the forehead and eyelashes. Tinnitus and frequent headache were reported. There was no history of eye trauma. Ophthalmologic examination revealed bilateral panuveitis and retinal detachment on the right eye. Histopathologic examination showed no melanin pigment in the basal layer. The patient was treated with systemic methyl-prednisolone and topical steroid creams. Prognosis is ad malam for ad sanam and ad cosmeticam.The diagnosis was based on AUS criteria and histopathologic examination. The precise etiology for VKHS is challenging to establish. Treatment required long term steroid administration and routine follow up to assess the progression of this disease.

Paper Citation

in Harvard Style

Hidayat E., Wulansari M., Sugianto Y., Damayanti G. and Astutik D. (2019). Vogt Koyanagi Harada Syndrome.In Proceedings of the 2nd International Conference on Tropical Medicine and Infectious Disease - Volume 1: ICTROMI, ISBN 978-989-758-469-5, pages 348-351. DOI: 10.5220/0009988503480351

in Bibtex Style

@conference{ictromi19,
author={Ernawati Hidayat and Milka Wulansari and Yosep Ferdinand Rahmat Sugianto and Galih Sari Damayanti and Dewi Kusuma Astutik},
title={Vogt Koyanagi Harada Syndrome},
booktitle={Proceedings of the 2nd International Conference on Tropical Medicine and Infectious Disease - Volume 1: ICTROMI,},
year={2019},
pages={348-351},
publisher={SciTePress},
organization={INSTICC},
doi={10.5220/0009988503480351},
isbn={978-989-758-469-5},
}

in EndNote Style

TY - CONF

JO - Proceedings of the 2nd International Conference on Tropical Medicine and Infectious Disease - Volume 1: ICTROMI,
TI - Vogt Koyanagi Harada Syndrome
SN - 978-989-758-469-5
AU - Hidayat E.
AU - Wulansari M.
AU - Sugianto Y.
AU - Damayanti G.
AU - Astutik D.
PY - 2019
SP - 348
EP - 351
DO - 10.5220/0009988503480351